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Results 1 to 25 of 74

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LE MODE D'EXCRETION URINAIRE DES MUCOPOLYOSIDES ACIDES CHEZ LES ENFANTS. I. MODE D'EXCRETION URINAIRE DES MUCOPOLYOSIDES ACIDES CHEZ LES ENFANTS NORMAUX DU SEXE MASCULINMINAMI R.1971; SAPPORO MED. J.; JAP.; DA. 1971; VOL. 40; NO 1-2; PP. 12-19; ABS. ANGL.; BIBL. 1P.1/2Serial Issue

A TRIAL MONTE CARLO TRAJECTORY CALCULATION OF THE RATE CONSTANTS FOR THE REACTIONS H2+I AND H2+I2MINAMI R; FUENO T.1979; CHEM. LETTERS; JPN; DA. 1979; NO 4; PP. 343-346; BIBL. 5 REF.Article

BASIC STUDY OF COAL LIQUEFACTION WITH DONOR SOLVENTHOSOI T; SUNAMI Y; HAYAKAWA K et al.1982; SUMITOMO KINZOKU; ISSN 0371-411X; JPN; DA. 1982-10; VOL. 34; NO 3; PP. 450-462; BIBL. 8 REF.Article

A STUDY OF UREA-SYNTHESIZING ENZYMES IN PRENATAL AND POSTNATAL HUMAN LIVEROYANAGI K; NAKAMURA K; SOGAWA H et al.1980; PEDIATR. RES.; USA; DA. 1980; VOL. 14; NO 3; PP. 236-241; BIBL. 16 REF.Article

AGE-DEPENDENT VARIATIONS OF LYSOSOMAL ENZYMES IN HUMAN LIVERMINAMI R; SATO S; KUDOH T et al.1979; TIHOKU J. EXPER. MED.; JPN; DA. 1979; VOL. 129; NO 1; PP. 65-70; BIBL. 9 REF.Article

ATYPICAL HURLER SYNDROME WITHOUT A-L-IDURONIDASE DEFICIENCY.ORII T; SUKEGAWA K; MINAMI R et al.1976; TOHOKU J. EXPER. MED.; JAP.; DA. 1976; VOL. 120; NO 2; PP. 113-123; BIBL. 14 REF.Article

CYSTINURIC HETEROZYGOTES AND CYSTINE-LOADING.MINAMI R; OLEK K; WARDENBACH P et al.1975; HUMANGENETIK; DTSCH.; DA. 1975; VOL. 29; NO 2; PP. 145-149; BIBL. 8 REF.Article

ETUDE D'EMULSIONS DANS LES SELS FONDUS. IV. LES SUSPENSIONS DE MG METALLIQUE DANS UN MELANGE DE MGCL2-KCL FONDUMINAMI R; NAKAJIMA T; WATANABE N et al.1975; NIPPON KAGAKU KAISHI; JAP.; DA. 1975; NO 11; PP. 1892-1895; ABS. ANGL.; BIBL. 13 REF.Article

DECREASE OF URINARY ACID MUCOPOLYSACCHARIDES IN HURLER'S SYNDROME AFTER PLASMA INFUSION = DIMINUTION DES MUCOPOLYSACCHARIDES ACIDES URINAIRES DANS LE SYNDROME DE HURLER APRES PERFUSION DE PLASMAORII T; YAMAGUCHI M; MINAMI R et al.1974; TOHOKU J. EXPER. MED.; JAP.; DA. 1974; VOL. 112; NO 4; PP. 385-387; BIBL. 8REF.Article

HYPERGLYCOPEPTIDURIA IN GENETIC MUCOLIPIDOSES = HYPERGLYCOPEPTIDURIE DANS LES MUCOLIPIDOSES GENETIQUESORII T; CHIBA T; MINAMI R et al.1974; TOHOKU J. EXPER. MED.; JAP.; DA. 1974; VOL. 112; NO 4; PP. 373-380; BIBL. 17REF.Article

A NEW TYPE OF MUCOLIPIDOSIS WITH BETA -GALACTOSIDASE DEFICIENCY AND GLYCOPEPTIDURIA = UN NOUVEAU TYPE DE MUCOLIPIDOSE AVEC DEFICIENCE DE BETA -GALACTOSIDASE ET GLYCOPEPTIDURIEORII T; MINAMI R; SUKEGAWA K et al.1972; TOHOKU J. EXPER. MED.; JAP.; DA. 1972; VOL. 107; NO 4; PP. 303-315; BIBL. 1P.Serial Issue

DIELECTRIE STUDY OF ALIPHATIC ESTERS IN CYCLOHEXANE SOLUTION AT THE FREQUENCY OF 100 GHZKANO Y; MINAMI R; TAKAHASHI H et al.1980; BULL. CHEM. SOC. JAP.; JPN; DA. 1980; VOL. 53; NO 3; PP. 642-644; BIBL. 12 REF.Article

GRADIENT SEPARATION OF NORMAL AND MALIGNANT CELLS. II: APPLICATION TO IN VIVO TUMOR DIAGNOSISMINAMI R; YOKOTA S; TEPLITZ RL et al.1978; ACTA CYTOL.; USA; DA. 1978; VOL. 22; NO 6; PP. 584-588; BIBL. 5 REF.Article

HYPERSARCOSINEMIA WITH CRANIOSTENOSIS-SYNDACTYLISM SYNDROME = HYPERSARCOSINEMIE AVEC SYNDROME DE CRANIOSTENOSE ET DE SYNDACTYLIEMINAMI R; OLEK K; WARDENBACH P et al.1975; HUMANGENETIK; DTSCH.; DA. 1975; VOL. 28; NO 2; PP. 167-171; BIBL. 7 REF.Article

PHENYLKETONURIA IN A PATIENT WITH CYSTINURIA. = PHENYLCETONURIE CHEZ UN PATIENT AVEC CYSTINURIEMINAMI R; OLEK K; WARDENBACH P et al.1975; HUMANGENETIK; DTSCH.; DA. 1975; VOL. 28; NO 4; PP. 319-324; BIBL. 12 REF.Article

VITAMIN D DEPENDENT RICKETS: DECREASED SENSITIVITY TO 1,25-DIHYDROXYVITAMIN DKUDOH T; KUMAGAI T; UETSUJI N et al.1981; EUR. J. PEDIATR.; ISSN 0340-6199; DEU; DA. 1981; VOL. 137; NO 3; PP. 307-311; BIBL. 10 REF.Article

A THEORETICAL APPROACH TO THE DIELECTRIC RELAXATION OF ALCOHOL SOLUTIONSMINAMI R; ITOH K; SATO H et al.1981; BULL. CHEM. SOC. JPN.; ISSN 0009-2673; JPN; DA. 1981; VOL. 54; NO 5; PP. 1320-1323; BIBL. 25 REF.Article

A THEORETICAL APPROACH TO THE DIELECTRIC RELAXATION OF LIQUID ALCOHOLSMINAMI R; ITOH K; TAKAHASHI H et al.1980; J. CHEM. PHYS.; ISSN 0021-9606; USA; DA. 1980; VOL. 73; NO 7; PP. 3396-3397; BIBL. 5 REF.Article

DUBIN-JOHNSON SYNDROME IN A NEONATENAKATA F; OYANAGI K; FUJIWARA M et al.1979; EUROP. J. PEDIATR.; DEU; DA. 1979; VOL. 132; NO 2; PP. 299-301; BIBL. 7 REF.Article

IDENTIFICATION OF KERATAN SULFATE IN LIVER AFFECTED BY MORQUIO SYNDROMEMINAMI R; ABO K; KUDOH T et al.1979; CLIN. CHIM. ACTA; NLD; DA. 1979; VOL. 93; NO 2; PP. 207-213; BIBL. 26 REF.Article

SPHINGOMYELINASE ACTIVITIES IN CULTURED SKIN FIBROBLASTS FROM PATIENTS WITH NIEMANN-PICK DISEASEMINAMI R; MATSUURA Y; NAKAMURA F et al.1979; HUM. GENET.; DEU; DA. 1979; VOL. 47; NO 2; PP. 159-167; BIBL. 16 REF.Article

LYSOSOMAL ACID HYDROLASES IN ESTABLISHED LYMPHOBLASTOID CELL LINES, TRANSFORMED BY EPSTEIN-BARR VIRUS FROM PATIENTS WITH GENETIC LYSOSOMAL STORAGE DISEASESMINAMI R; WATANABE Y; KUDOH T et al.1978; HUM. GENET.; DEU; DA. 1978; VOL. 44; NO 1; PP. 79-87; BIBL. 11 REF.Article

INFLUENCE OF FRESH PLASMA INFUSIONS ON PATIENTS WITH GENETIC MUCOPOLYSACCHARIDOSIS = ACTION DES PERFUSIONS DE PLASMA FRAIS CHEZ DES MALADES ATTEINTS DE MUCOPOLYSACCHARIDOSES D'ORIGINE GENETIQUEORII T; YAMAGUCHI M; MINAMI R et al.1974; TOHOKU J. EXPER. MED.; JAP.; DA. 1974; VOL. 114; NO 4; PP. 385-392; BIBL. 13REF.Article

A THEORETICAL APPROACH TO THE DIELECTRIC RELAXATION OF ALCOHOL SOLUTIONS. II: THE EFFECT OF DILUTION WITH INERT SOLVENTS ON THE PRINCIPAL RELAXATION TIMES OF PRIMARY ALCOHOLSMINAMI R; ITOH K; TAKAHASHI H et al.1981; BULL. CHEM. SOC. JPN.; ISSN 0009-2673; JPN; DA. 1981; VOL. 54; NO 12; PP. 3684-3687; BIBL. 18 REF.Article

FLUOROMETRIC MEASUREMENT OF ALPHA -L-IDURONIDASE ACTIVITY USING 4-METHYLUMBELLIFERYL-ALPHA -L-IDURONIDEMINAMI R; WATANABE Y; KUDOH T et al.1980; TOHOKU J. EXPER. MED.; JPN; DA. 1980; VOL. 130; NO 4; PP. 381-384; BIBL. 7 REF.Article

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